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DeCS
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Descriptor English:
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Polyendocrinopathies, Autoimmune
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Descriptor Spanish:
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Poliendocrinopatías Autoinmunes
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Descriptor Portuguese:
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Poliendocrinopatias Auto-Imunes
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Synonyms English:
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Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
Autoimmune Syndrome Type I, Polyglandular
Autoimmune Syndrome Type II, Polyglandular
Polyglandular Type I Autoimmune Syndrome
Polyglandular Type II Autoimmune Syndrome
Schmidt's Syndrome
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Tree Number:
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C19.787
C20.111.750
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Definition English:
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Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present. |
Indexing Annotation English:
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do not coordinate with specific endocrine disease term or CANDIDIASIS unless particularly discussed
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History Note English:
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1992
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Allowable Qualifiers English:
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Record Number:
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29879
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Unique Identifier:
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D016884
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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